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Hyperparathyroidism ICD-10 Code: E21.3

Last updated: January 4, 2026

Hyperparathyroidism is coded based on type: primary, secondary, or tertiary.

Hyperparathyroidism Code Selection

CodeDescriptionCause
E21.0Primary hyperparathyroidismParathyroid adenoma, hyperplasia
E21.1Secondary hyperparathyroidism, NECChronic kidney disease
E21.2Other hyperparathyroidismTertiary HPT
E21.3Hyperparathyroidism, unspecifiedType not documented

Secondary HPT Exclusions

E21.1 excludes:

  • Secondary hyperparathyroidism of renal origin -> N25.81
CKD with Secondary HPTCode
CKD stage 3-5 with 2 deg HPTN18.x + N25.81
ESRD on dialysis with 2 deg HPTN18.6 + N25.81
Non-renal secondary HPTE21.1

Associated Conditions

ConditionCode
HypercalcemiaE83.52
HypophosphatemiaE83.39
Kidney stonesN20.x
OsteoporosisM81.0/M80.x
Parathyroid adenomaD35.1
Parathyroid carcinomaC75.0

Coding Tips

  1. Query type: Primary vs secondary significantly affects treatment
  2. Renal secondary HPT: Use N25.81, not E21.1
  3. Hypercalcemia: Code E83.52 as manifestation
  4. Post-parathyroidectomy: Use E89.2 for postprocedural hypoparathyroidism

Primary vs Secondary vs Tertiary

TypePTHCalciumCause
PrimaryHighHighAdenoma, hyperplasia
SecondaryHighLow/NormalCKD, vitamin D deficiency
TertiaryHighHighLong-standing secondary
CodeDescription
E20.0Idiopathic hypoparathyroidism
E89.2Postprocedural hypoparathyroidism
N25.81Secondary hyperparathyroidism of renal origin
D35.1Benign neoplasm of parathyroid gland

Frequently Asked Questions

What is the ICD-10 code for hyperparathyroidism?

E21.0 for primary hyperparathyroidism, E21.1 for non-renal secondary, N25.81 for renal secondary, or E21.3 for unspecified.

How do I code secondary hyperparathyroidism with CKD?

Use the CKD code (N18.x) plus N25.81 (Secondary hyperparathyroidism of renal origin). Do NOT use E21.1 for renal secondary HPT.

What's the difference between primary and secondary hyperparathyroidism?

Primary (E21.0) is autonomous PTH overproduction (adenoma). Secondary (E21.1/N25.81) is reactive to low calcium or CKD. Primary causes hypercalcemia; secondary often doesn't.

Related Resources

Last updated: January 2026. Code data reflects ICD-10-CM 2026 version. This guide is for educational purposes only. Always verify codes against current official guidelines.