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Multiple Myeloma ICD-10 Code: C90.00

Last updated: January 4, 2026

Multiple myeloma is coded using C90.0x with a 5th character for remission status.

Multiple Myeloma Code Selection

CodeDescription
C90.00Multiple myeloma not having achieved remission
C90.01Multiple myeloma in remission
C90.02Multiple myeloma in relapse

Remission Status Guide

StatusCodeDocumentation
Active diseaseC90.00New diagnosis, ongoing treatment, not in remission
RemissionC90.01Complete or partial remission documented
RelapseC90.02Disease recurrence after remission

Other Plasma Cell Neoplasms

CodeDescription
C90.10Plasma cell leukemia not in remission
C90.20Extramedullary plasmacytoma not in remission
C90.30Solitary plasmacytoma not in remission
D47.Z9MGUS (monoclonal gammopathy of undetermined significance)

Complication Coding

ComplicationCode
Pathologic fractureM84.5x + C90.0x
HypercalcemiaE83.52 + C90.0x
Renal insufficiencyN18.x + C90.0x
AnemiaD63.0 (anemia in neoplastic disease)
Bone lesionsCode specific site

Coding Tips

  1. Remission status: Always verify from documentation; don't assume
  2. Personal history: Use Z85.79 after cure (rare in myeloma)
  3. Chemotherapy encounter: Code C90.0x as primary with Z51.11
  4. Bone pain: Code both myeloma and bone lesion site

CRAB Criteria (Clinical Reference)

FindingMeaningCode
CCalcium elevationE83.52
RRenal insufficiencyN18.x
AAnemiaD63.0
BBone lesionsSite-specific

Frequently Asked Questions

What is the ICD-10 code for multiple myeloma?

C90.00 (Multiple myeloma not having achieved remission) is the most common code. Use C90.01 for remission or C90.02 for relapse.

How do I code multiple myeloma in remission?

Use C90.01 (Multiple myeloma in remission). Documentation must specifically state the patient is in complete or partial remission.

What's the difference between myeloma and MGUS?

Multiple myeloma (C90.0x) is malignant. MGUS (D47.Z9) is premalignant. MGUS doesn't have CRAB criteria (hypercalcemia, renal failure, anemia, bone lesions).

Related Resources

Last updated: January 2026. Code data reflects ICD-10-CM 2026 version. This guide is for educational purposes only. Always verify codes against current official guidelines.