D812026

Non-billable

Combined immunodeficiencies

Clinical Notes

  • autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

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Related Codes
D81Combined immunodeficiencies
D81.0Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3Adenosine deaminase [ADA] deficiency
D81.30Adenosine deaminase deficiency, unspecified
D81.31Severe combined immunodeficiency due to adenosine deaminase deficiency
D81.32Adenosine deaminase 2 deficiency
D81.39Other adenosine deaminase deficiency
D81.4Nezelof's syndrome
D81.5Purine nucleoside phosphorylase [PNP] deficiency
D81.6Major histocompatibility complex class I deficiency
D81.7Major histocompatibility complex class II deficiency
D81.8Other combined immunodeficiencies
D81.81Biotin-dependent carboxylase deficiency
D81.810Biotinidase deficiency
D81.818Other biotin-dependent carboxylase deficiency
D81.819unspecified
D81.82Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
D81.89Other combined immunodeficiencies
D81.9Combined immunodeficiency, unspecified