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E712026

Non-billable

Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

Clinical Notes

    From E70-E88
    • Androgen insensitivity syndrome (E34.5-)
    • Congenital adrenal hyperplasia (E25.0)
    • Hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan syndrome (Q87.4-)
    • 5-alpha-reductase deficiency (E29.1)
    From E00-E89
    • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

    Frequently Asked Questions

    Code Hierarchy
    Metabolic disorders (E70-E88)
    Disorders of aromatic amino-acid metabolism
    E71
    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
    Maple-syrup-urine disease
    Other disorders of branched-chain amino-acid metabolism
    Disorder of branched-chain amino-acid metabolism, unspecified
    ...fatty-acid metabolism
    ...carnitine metabolism
    Peroxisomal disorders
    Other disorders of amino-acid metabolism
    Lactose intolerance
    Other disorders of carbohydrate metabolism
    Disorders of sphingolipid metabolism and other lipid storage disorders
    Disorders of glycosaminoglycan metabolism
    Disorders of glycoprotein metabolism
    Disorders of lipoprotein metabolism and other lipidemias
    Disorders of purine and pyrimidine metabolism
    Disorders of porphyrin and bilirubin metabolism
    Disorders of mineral metabolism
    Cystic fibrosis
    Amyloidosis
    Volume depletion
    Other disorders of fluid, electrolyte and acid-base balance
    Other and unspecified metabolic disorders

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    Related MS-DRGs
    61,940 Medicare hospitalizations across 1 DRG for codes in E71

    Top DRGs associated with codes in this category:

    642INBORN AND OTHER DISORDERS OF METABOLISM61,940
    Official Guidelines
    Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

    Official coding guidelines for E00-E89

    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism - ICD-10 Code E71 | FindICD10