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E752026

Non-billable

Disorders of sphingolipid metabolism and other lipid storage disorders

Clinical Notes

  • Mucolipidosis, types I-III (E77.0-E77.1)
  • Refsum's disease (G60.1)
From E70-E88
  • Androgen insensitivity syndrome (E34.5-)
  • Congenital adrenal hyperplasia (E25.0)
  • Hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From E00-E89
  • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Frequently Asked Questions

Code Hierarchy
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
GM2 gangliosidosis
Other and unspecified gangliosidosis
Other sphingolipidosis
Sphingolipidosis, unspecified
Neuronal ceroid lipofuscinosis
Other lipid storage disorders
Lipid storage disorder, unspecified

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Related MS-DRGs
591,390 Medicare hospitalizations across 3 DRGs for codes in E75

Top DRGs associated with codes in this category:

057DEGENERATIVE NERVOUS SYSTEM DISORDERS WITHOUT MCC370,510
056DEGENERATIVE NERVOUS SYSTEM DISORDERS WITH MCC201,320
642INBORN AND OTHER DISORDERS OF METABOLISM19,560
Official Guidelines
Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

Official coding guidelines for E00-E89

Disorders of sphingolipid metabolism and other lipid storage disorders - ICD-10 Code E75 | FindICD10