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E762026

Non-billable

Disorders of glycosaminoglycan metabolism

Clinical Notes

    From E70-E88
    • Androgen insensitivity syndrome (E34.5-)
    • Congenital adrenal hyperplasia (E25.0)
    • Hemolytic anemias attributable to enzyme disorders (D55.-)
    • Marfan syndrome (Q87.4-)
    • 5-alpha-reductase deficiency (E29.1)
    From E00-E89
    • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

    Frequently Asked Questions

    Code Hierarchy
    E76
    Disorders of glycosaminoglycan metabolism
    Mucopolysaccharidosis, type I
    Mucopolysaccharidosis, type II
    Other mucopolysaccharidoses
    Mucopolysaccharidosis, unspecified
    Other disorders of glucosaminoglycan metabolism
    Glucosaminoglycan metabolism disorder, unspecified

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    Related MS-DRGs
    19,560 Medicare hospitalizations across 1 DRG for codes in E76

    Top DRGs associated with codes in this category:

    642INBORN AND OTHER DISORDERS OF METABOLISM19,560
    Official Guidelines
    Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

    Official coding guidelines for E00-E89

    Disorders of glycosaminoglycan metabolism - ICD-10 Code E76 | FindICD10