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E782026

Non-billable

Disorders of lipoprotein metabolism and other lipidemias

Clinical Notes

  • Sphingolipidosis (E75.0-E75.3)
From E70-E88
  • Androgen insensitivity syndrome (E34.5-)
  • Congenital adrenal hyperplasia (E25.0)
  • Hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From E00-E89
  • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Frequently Asked Questions

Code Hierarchy
Metabolic disorders (E70-E88)
Disorders of aromatic amino-acid metabolism
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Other disorders of amino-acid metabolism
Lactose intolerance
Other disorders of carbohydrate metabolism
Disorders of sphingolipid metabolism and other lipid storage disorders
Disorders of glycosaminoglycan metabolism
Disorders of glycoprotein metabolism
E78
Disorders of lipoprotein metabolism and other lipidemias
Pure hypercholesterolemia
Pure hyperglyceridemia
Mixed hyperlipidemia
Hyperchylomicronemia
Other hyperlipidemia
Hyperlipidemia, unspecified
Lipoprotein deficiency
...bile acid and cholesterol metabolism
Other disorders of lipoprotein metabolism
Disorder of lipoprotein metabolism, unspecified
Disorders of purine and pyrimidine metabolism
Disorders of porphyrin and bilirubin metabolism
Disorders of mineral metabolism
Cystic fibrosis
Amyloidosis
Volume depletion
Other disorders of fluid, electrolyte and acid-base balance
Other and unspecified metabolic disorders

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Related MS-DRGs
50,062 Medicare hospitalizations across 4 DRGs for codes in E78

Top DRGs associated with codes in this category:

642INBORN AND OTHER DISORDERS OF METABOLISM22,820
565OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC13,822
564OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC10,756
566OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC2,664
Official Guidelines
Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

Official coding guidelines for E00-E89

Disorders of lipoprotein metabolism and other lipidemias - ICD-10 Code E78 | FindICD10