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E782026

Non-billable

Disorders of lipoprotein metabolism and other lipidemias

Clinical Notes

  • Sphingolipidosis (E75.0-E75.3)
From E70-E88
  • Androgen insensitivity syndrome (E34.5-)
  • Congenital adrenal hyperplasia (E25.0)
  • Hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From E00-E89
  • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Frequently Asked Questions

Code Hierarchy
E78
Disorders of lipoprotein metabolism and other lipidemias
Pure hypercholesterolemia
Pure hyperglyceridemia
Mixed hyperlipidemia
Hyperchylomicronemia
Other hyperlipidemia
Hyperlipidemia, unspecified
Lipoprotein deficiency
...bile acid and cholesterol metabolism
Other disorders of lipoprotein metabolism
Disorder of lipoprotein metabolism, unspecified

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Related MS-DRGs
50,062 Medicare hospitalizations across 4 DRGs for codes in E78

Top DRGs associated with codes in this category:

642INBORN AND OTHER DISORDERS OF METABOLISM22,820
565OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH CC13,822
564OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITH MCC10,756
566OTHER MUSCULOSKELETAL SYSTEM AND CONNECTIVE TISSUE DIAGNOSES WITHOUT CC/MCC2,664
Official Guidelines
Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

Official coding guidelines for E00-E89

Disorders of lipoprotein metabolism and other lipidemias - ICD-10 Code E78 | FindICD10