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E882026

Non-billable

Other and unspecified metabolic disorders

Clinical Notes

  • Histiocytosis X (chronic) (C96.6)
From E70-E88
  • Androgen insensitivity syndrome (E34.5-)
  • Congenital adrenal hyperplasia (E25.0)
  • Hemolytic anemias attributable to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4-)
  • 5-alpha-reductase deficiency (E29.1)
From E00-E89
  • Transitory endocrine and metabolic disorders specific to newborn (P70-P74)

Frequently Asked Questions

Code Hierarchy
Metabolic disorders (E70-E88)
Disorders of aromatic amino-acid metabolism
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Other disorders of amino-acid metabolism
Lactose intolerance
Other disorders of carbohydrate metabolism
Disorders of sphingolipid metabolism and other lipid storage disorders
Disorders of glycosaminoglycan metabolism
Disorders of glycoprotein metabolism
Disorders of lipoprotein metabolism and other lipidemias
Disorders of purine and pyrimidine metabolism
Disorders of porphyrin and bilirubin metabolism
Disorders of mineral metabolism
Cystic fibrosis
Amyloidosis
Volume depletion
Other disorders of fluid, electrolyte and acid-base balance
E88
Other and unspecified metabolic disorders
Disorders of plasma-protein metabolism, not elsewhere classified
Lipodystrophy, not elsewhere classified
Lipomatosis, not elsewhere classified
Tumor lysis syndrome
Mitochondrial metabolism disorders
Other specified metabolic disorders
Metabolic disorder, unspecified
Wasting disease (syndrome) due to underlying condition

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Related MS-DRGs
234,482 Medicare hospitalizations across 5 DRGs for codes in E88

Top DRGs associated with codes in this category:

683RENAL FAILURE WITH CC82,015
682RENAL FAILURE WITH MCC80,197
642INBORN AND OTHER DISORDERS OF METABOLISM26,080
673OTHER KIDNEY AND URINARY TRACT PROCEDURES WITH MCC14,083
684RENAL FAILURE WITHOUT CC/MCC7,199
Official Guidelines
Chapter 4: Endocrine, Nutritional, and Metabolic Diseases

Official coding guidelines for E00-E89

Other and unspecified metabolic disorders - ICD-10 Code E88 | FindICD10